Disseminated juvenile xanthogranulomas with systemic involvement: A rare presentation

Abstract

Juvenile xanthogranuloma is a self-healing non-Langerhans cell histiocytosis. It primarily manifests with cutaneous lesions which may have systemic associations. We report a case of a 6-month-old child who presented with multiple orangish papules and nodules all over the body with eye and liver involvement, which is a rare entity. The diagnosis was confirmed with dermoscopy and histopathological assessment, including immunohistochemical study. He responded to medical line of therapy.

Keywords

• Juvenile xanthogranuloma
• non-Langerhans cell histiocytosis
• xanthogranulomas with systemic involvement