Fetal Unguarded Mitral Valve Orifice, Aortic Atresia, and Severe Left Heart Enlargement

Lisa W. Howley, MD; Janette Strasburger, MD; Joseph J. Maleszewski, MD; Saul Snowise, MD; Amy Lund, CNP; Andrew Schneider, MD; Robroy MacIver, MD; Erik Edens, MD; Stephanie Eyerly-Webb, PhD; Norman H. Silverman, MD, DSc(Med)

JACC: Case Reports (Feb 2021)

Fetal Unguarded Mitral Valve Orifice, Aortic Atresia, and Severe Left Heart Enlargement

Lisa W. Howley, MD,
Janette Strasburger, MD,
Joseph J. Maleszewski, MD,
Saul Snowise, MD,
Amy Lund, CNP,
Andrew Schneider, MD,
Robroy MacIver, MD,
Erik Edens, MD,
Stephanie Eyerly-Webb, PhD,
Norman H. Silverman, MD, DSc(Med)

Affiliations

Lisa W. Howley, MD: Division of Cardiology, Department of Pediatrics, The Children’s Heart Clinic, Children's Minnesota, Minneapolis, Minnesota, USA; Midwest Fetal Care Center, Children's Minnesota, Minneapolis, Minnesota, USA; Address for correspondence: Dr. Lisa W. Howley, Fetal Cardiology Program, Division of Cardiology, The Children's Heart Clinic, Children's Minnesota, 2530 Chicago Avenue S, Suite 500, Minneapolis, Minnesota 55404, USA.
Janette Strasburger, MD: Division of Cardiology, Department of Pediatrics, Children’s Hospital of Wisconsin, Milwaukee, Wisconsin, USA
Joseph J. Maleszewski, MD: Department of Laboratory Medicine and Pathology, Mayo Clinic, Rochester, Minnesota, USA
Saul Snowise, MD: Midwest Fetal Care Center, Children's Minnesota, Minneapolis, Minnesota, USA
Amy Lund, CNP: Division of Cardiology, Department of Pediatrics, The Children’s Heart Clinic, Children's Minnesota, Minneapolis, Minnesota, USA; Midwest Fetal Care Center, Children's Minnesota, Minneapolis, Minnesota, USA
Andrew Schneider, MD: Division of Cardiology, Department of Pediatrics, The Children’s Heart Clinic, Children's Minnesota, Minneapolis, Minnesota, USA
Robroy MacIver, MD: Division of Cardiac Surgery, The Children’s Heart Clinic, Children's Minnesota, Minneapolis, Minnesota, USA
Erik Edens, MD: Division of Cardiology, Department of Pediatrics, The Children’s Heart Clinic, Children's Minnesota, Minneapolis, Minnesota, USA
Stephanie Eyerly-Webb, PhD: Midwest Fetal Care Center, Children's Minnesota, Minneapolis, Minnesota, USA
Norman H. Silverman, MD, DSc(Med): Division of Cardiology, Department of Pediatrics, University of California, San Francisco, California, USA

Journal volume & issue: Vol. 3, no. 2
pp. 206 – 211

Abstract

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Unguarded mitral valve orifice is a rare disease with only 7 described cases in the literature. We describe the first known case of unguarded mitral valve orifice with normal segmental cardiac anatomy, severe left ventricular dilatation and dysfunction, aortic atresia, and atrial flutter. (Level of Difficulty: Advanced.)

Published in JACC: Case Reports

ISSN: 2666-0849 (Online)
Publisher: Elsevier
Country of publisher: United States
LCC subjects: Medicine: Internal medicine: Specialties of internal medicine: Diseases of the circulatory (Cardiovascular) system
Website: https://www.journals.elsevier.com/jacc-case-reports

About the journal

Abstract

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