Clear cell sarcoma arising from paraspinal ligament of thoracic spine: Report of an unusual case

Abstract

Clear cell sarcoma (CCS) is an unusual but aggressive soft-tissue tumor with an incidence of <1% of all soft-tissue sarcomas. It was previously termed “malignant melanoma of soft parts” due to its resemblance clinically and morphologically. Normally CCS is seen in patients aged 20–40 years. A rare case of CCS of paraspinal ligament in a 5-year-old boy is being reported. Histopathology and immunohistochemistry markers confirmed the diagnosis. The present case is unique since the entity itself is rare and also due to its occurrence in a child.

Keywords

• Clear cell sarcoma
• melanoma
• paraspinal ligament
• soft tissue