Baby with neonatal systemic juvenile xanthogranuloma born within a cross-cousin marriage

Abstract

Juvenile xanthogranuloma is a non-Langerhans cell histiocytosis seen most commonly in childhood and adolescence. Extracutaneous involvement is rare. We report an interesting and extremely rare case of systemic (skin, lung, spleen, and colon) “juvenile xanthogranuloma” in the neonatal period. Our case was the first ever reported case born to a cross-cousin marriage.

Keywords

• juvenile xanthogranuloma
• non-Langerhans cell histiocytosis