Localized Pseudoxanthomatous Mastocytosis of Vulva

Abstract

Cutaneous mastocytosis (CM) is a mast cell proliferative disorder that is common in the pediatric age group. Common entities are urticaria pigmentosa, solitary mastocytoma, telangiectasia macularis eruptive perstans. and diffuse CM. Pseudoxanthomatous mastocytosis presents in the form of yellowish nodular lesion resembling xanthoma and is a rare variant and not reported much in the literature. We, hereby report a rare case of localized vulvar pseudoxanthomatous mastocytosis in a 10-year-old female child.

Keywords

• cutaneous mastocytosis
• localized vulvar pseudoxanthomatous mastocytosis
• pediatric mastocytosis