Saudi Journal of Kidney Diseases and Transplantation (Jan 2017)

A rare cardiac manifestation in autosomal-dominant polycystic kidney disease

  • Meriam Hajji,
  • Hela Jebali,
  • Khadija Mzoughi,
  • Ihssen Zairi,
  • Rania Kheder,
  • Lilia Ben Fatma,
  • Lamia Rais,
  • Rokaya Kadouri,
  • Sinda Kraiem,
  • Wided Smaoui,
  • Madiha Krid,
  • Soumaya Beji,
  • Karim Zouaghi

DOI
https://doi.org/10.4103/1319-2442.220844
Journal volume & issue
Vol. 28, no. 6
pp. 1443 – 1446

Abstract

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Autosomal-dominant polycystic kidney disease (ADPKD) is a systemic disorder associated with various extrarenal complications. There is little information regarding the occurrence and distribution of cardiovascular abnormalities during the course of ADPKD. The major cardiovascular complications of ADPKD include valvulopathies and vascular ectasia. Aneurysm of the atrial septum (ASA) is a very rare manifestation in ADPKD. A 37-year-old woman who was diagnosed with ADPKD was admitted to our hospital for advanced renal failure. Pelvic computed tomography revealed multiple variable-sized cysts in both kidneys. Trans-thoracic echocardiography showed ASA while the patient was completely asymptomatic.