SECONDARY AND TERTIARY PROFILAXY OF THE MOYAMOYA DISEASE IN CHILDHOOD CASE PRESENTATION

Abstract

The Moyamoya syndrome (also known as the Moyamoya disease) consists of a series of malformations and congenital modifications of the cerebral arteries and occlusions and narrowing of the terminal carotid artery bifurcation. The term Moyamoya comes from the Japanese language and means "puff smoke". This describes the arteriography of cerebral artery changes, which emit numerous small-diameter collateral vessels with fragile walls. The diagnosis of Moyamoya disease is established after excluding other genetic or congenital causes of such vascular malformations. These vessels with increased fragility often have parietal lesions at increased risk of rupture and secondary stroke. In the present paper we aim to present the case of a child diagnosed with the Moyamoya disease who suffered two vascular accidents and is currently in the recovery process. The treatment is complex and consists of surgery and rehabilitation. Depending on the location of the cerebral malformations, clinical manifestations are diverse. In the present case, they are motor, but the child also has speech disorders, even if the intelligence is preserved.

Keywords

• Vascular malformations
• child stroke
• rehabilitation