Type II Abernethy Malformation in a Patient with Primary Budd-Chiari Syndrome

Abstract

Budd-Chiari syndrome (BCS) is a heterogeneous group of disorders characterized by hepatic venous outflow obstruction. Abernethy malformation is a congenital vascular malformation defined by diversion of portal blood away from the liver. Both conditions are rare vascular diseases. We report here the first case of a patient with combined type II Abernethy malformation and BCS from China. The inferior vena cava obstruction was treated with percutaneous balloon angioplasty; close follow-up was elected for the Abernethy malformation.

Keywords

• Congenital porto-systemic shunt
• Hepatic venous outflow obstruction
• Inferior vena cava
• Angiography