Indian Journal of Ophthalmology (Jan 2014)
An unusual combination of Unilateral Orbital Plexiform Neurofibroma in a patient with oculocutaneous albinism
- J Saravanan,
- A Rajendraprasad,
- S Priyadharshni
Affiliations
- J Saravanan
- A Rajendraprasad
- S Priyadharshni
- DOI
- https://doi.org/10.4103/0301-4738.136259
- Journal volume & issue
-
Vol. 62,
no. 6
pp. 735 – 737
Abstract
A 70-year-old female patient presented with proptosis of right eye for the past 15 days and defective vision in both eyes since birth. She was found to have eccentric painful proptosis of right eye along with features of oculocutaneous albinism. Eccentric proptosis was due to an orbital mass which proved to be a plexiform neurofibroma by histopathological examination. The case is presented for its rarity, as an isolated orbital plexiform neurofibroma without the systemic features of neurofibromatosis is rare and its coincidental presentation with oculocutaneous albinism is yet rare and has not been reported so far.
Keywords
- Color Doppler imaging
- hypertensive retinopathy
- resistive index
- Conjunctival graft
- primary pterygium
- recurrent pterygium
- Intraocular pressure
- singleton pregnancy
- the number of fetuses
- twin pregnancy
- Accommodation
- agreement
- amplitude of accommodation
- push-up method
- Intraocular lens
- non-sclera flap
- transscleral pars plana suture fixation
- Axial length
- formulas
- lens
- power
- short eyes
- Acquired esotropia
- favourable outcome
- stereopsis
- Diabetic retinopathy
- enzyme-linked immunosorbent assay
- immunology
- interleukin-1β
- interleukin-10
- proliferative
- Polypoidal choroidal vasculopathy
- preferential hyperacuity perimetry
- spectral-domain optical coherence tomography
- Microincisional vitreous surgery
- retained intraocular foreign bodies
- transconjunctival sutureless vitrectomy
- AS-OCT
- bleb morphology
- trabeculectomy
- Horizontal muscle surgery
- inferior oblique muscle recession surgery
- macular thickness
- optical coherence tomography
- Ganglion cell complex
- optical coherence tomography
- retinal nerve fiber layer
- type 2 diabetes
- Color vision
- color vision testing
- FM 100-Hue
- Ishihara
- Bilateral
- monosymptomatic optic neuritis
- Mycoplasma pneumoniae
- retro-bulbar optic neuritis
- Cavernous sinus involvement
- chasmal involvement
- optic atrophy
- optic nerve sheath meningioma
- Dicotyledones
- pterygium surgery
- subconjunctival foreign body
- uveal prolase
- Choroiodal melanoma
- endoresection
- vitrectomy
- Acrylic lens
- complication
- ectopic lens
- phacoemulsification
- Oculocutaneous albinism
- orbital plexiform neurofibroma
- proptosis
