Complete and Incomplete Pentalogy of Cantrell

Abstract

Pentalogy of Cantrell (PC) is a malformation characterized by defects in the ventral abdominal wall, lower sternum, diaphragmatic pericardium, anterior diaphragm associated with omphalocele, thoraco-abdominal ectopia cordis, diaphragmatic hernia, and intracardiac abnormalities. PC is stratified as complete or incomplete and we present both the complete and incomplete forms.

Keywords

• pentalogy of cantrell
• omphalocele
• ectopia cordis
• congenital heart disease