Congenitally “Inverted” Pulmonary Valve in Tetralogy of Fallot

Simone Jhaveri, MD; Ira Parness, MD; Tal Geva, MD; Matthew J. Bock, MD; Barry Love, MD; Shubhika Srivastava, MBBS

JACC: Case Reports (Apr 2020)

Congenitally “Inverted” Pulmonary Valve in Tetralogy of Fallot

Simone Jhaveri, MD,
Ira Parness, MD,
Tal Geva, MD,
Matthew J. Bock, MD,
Barry Love, MD,
Shubhika Srivastava, MBBS

Affiliations

Simone Jhaveri, MD: Department of Pediatric Cardiology, Icahn School of Medicine at Mount Sinai, New York, New York; Address for correspondence: Dr. Simone Jhaveri, Icahn School of Medicine at Mount Sinai, One Gustave L. Levy Place, Annenberg 3-50, New York, New York 10029.
Ira Parness, MD: Department of Pediatric Cardiology, Icahn School of Medicine at Mount Sinai, New York, New York
Tal Geva, MD: Department of Cardiology, Boston Children's Hospital, Boston, Massachusetts; Department of Pediatrics, Harvard Medical School, Boston, Massachusetts
Matthew J. Bock, MD: Department of Pediatric Cardiology, Loma Linda University Children’s Health, Loma Linda, California
Barry Love, MD: Department of Pediatric Cardiology, Icahn School of Medicine at Mount Sinai, New York, New York
Shubhika Srivastava, MBBS: Department of Pediatric Cardiology, Icahn School of Medicine at Mount Sinai, New York, New York

Journal volume & issue: Vol. 2, no. 4
pp. 544 – 546

Abstract

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A cyanotic neonate with tetralogy of Fallot was found to have a congenitally inverted pulmonary valve. Diagnosis was made via echocardiography and cardiac catheterization. The valve opened retrograde into the right ventricle, which allowed severe regurgitation and prevented anterograde flow. This report is the first description of this anomaly in medical literature. (Level of Difficulty: Intermediate.)

Published in JACC: Case Reports

ISSN: 2666-0849 (Online)
Publisher: Elsevier
Country of publisher: United States
LCC subjects: Medicine: Internal medicine: Specialties of internal medicine: Diseases of the circulatory (Cardiovascular) system
Website: https://www.journals.elsevier.com/jacc-case-reports

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Abstract

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