Journal of Cardiothoracic Surgery (Apr 2011)

Successful surgical excision of primary right atrial angiosarcoma

  • van der Horst Iwan CC,
  • Suurmeijer Albert JH,
  • Willems Tineke P,
  • Lexis Chris PH,
  • Bouma Wobbe,
  • Ebels Tjark,
  • Mariani Massimo A

DOI
https://doi.org/10.1186/1749-8090-6-47
Journal volume & issue
Vol. 6, no. 1
p. 47

Abstract

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Abstract Primary cardiac angiosarcoma is a rare and aggressive tumor with a high incidence of metastatic spread (up to 89%) at the time of diagnosis, which restricts the indication for surgical resection to a small number of patients. We report the case of a 50-year old Caucasian woman with non-metastatic primary right atrial angiosarcoma, who underwent successful surgical excision of the tumor (with curative intent) and reconstruction of the right atrium with a porcine pericardial patch. However, after a symptom-free survival of five months the patient presented with bone and liver metastases without evidence of local tumor recurrence.