Juvenile xanthogranuloma of the cerebellopontine angle: A case report and review of the literature

Abstract

Juvenile xanthogranuloma (JXG) is a non-Langerhans cell histiocytosis, most often presenting with skin lesions of the head, neck, and upper trunk. Intracranial presentations have been previously described, however, due to its rarity, treatment algorithms have not been developed. The current study presents the case of a JXG of the cerebellopontine angle in a 17-month-old male and a review of the current literature with management options. Keywords: Juvenile xanthogranuloma, Histiocytosis, Cerebellopontine angle