Recent advance on the treatment of neurofibromatosis type 2 ⁃ associated vestibular schwannoma

Abstract

Neurofibromatosis type 2 (NF2) is an autosomal dominant inherited diseases. NF2 patients suffer a high mortality and disability rate. Bilateral vestibular schwannoma play an important role in its diagnosis and treatment. The balance of treatment and life quality is the key factor in the treatment of NF2⁃associated vestibular schwannoma. This review summarized the recent advance of monitoring before treatment, treatment strategies and hearing reconstruction in NF2⁃associated vestibular schwannoma, in order to provide reference for clinical diagnosis and treatment.

Keywords

• neurofibromatosis 2
• neuroma
• acoustic
• review