Korean Journal of Pediatrics (Nov 2010)

Perivascular epithelioid cell tumor (PEComa) of the ascending colon: the implication of IFN-α2b treatment

  • Sun Ju Park,
  • Dong Kyun Han,
  • Hee Jo Baek,
  • Sang Young Chung,
  • Jong Hee Nam,
  • Hoon Kook,
  • Tai Ju Hwang

DOI
https://doi.org/10.3345/kjp.2010.53.11.975
Journal volume & issue
Vol. 53, no. 11
pp. 975 – 978

Abstract

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A 7-year-old boy presented with hematochezia and abdominal pain. A 3.7-cm-sized mass was identified in the ascending colon by abdominal computed tomography and colonoscopy. The patient underwent surgical resection. Pathological examination revealed a low-grade perivascular epithelioid cell tumor (PEComa). PEComa in the colon is very rare. Only a few cases have been reported so far. An effective treatment method for this rare tumor has not been established yet. The patient received adjuvant interferon-α immunotherapy for 1 year. He has been tumor-free for 26 months since the initial diagnosis. This report is the first documented case of the use of interferon-α for pediatric PEComa of the colon.

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