Abernethy syndrome, a rare cause of hypoxemia: A case report

Abstract

Abernethy syndrome (congenital extrahepatic portosystemic shunt (CEPS II)) as an etiology of hepatopulmonary syndrome (HPS) is uncommon. The severe hypoxemia and its consequences become incapacitating for the patient. Early shunt closure resolves hypoxemia and clinical symptomatology and prevents irreversible changes in pulmonary vasculature.

Keywords

• Abernethy syndrome
• cyanosis
• hepatopulmonary syndrome
• portosystemic shunt