Pain: A Necessary Evil? (Anesthetic Management of Congenital Pain Insensitivity Syndrome)

Abstract

Congenital insensitivity to pain with anhidrosis (CIPA) is a rare autosomal disorder. It is characterized by systemic insensitivity to pain, unexplained fever, and psychiatric manifestations. Anesthetic management of these cases is a challenge to the anesthetist due to the various implications associated with it. In this case report, we describe the anesthetic management of a 3-year-old child with CIPA and report the implications and challenges faced.

Keywords

• autonomic dysfunction
• congenital insensitivity
• congenital insensitivity to pain with anhidrosis
• pain