Heart Vessels and Transplantation (Jun 2023)

Case report of symptomatic very late presentation of ALCAPA syndrome: from AL-CAPONE to Robin Hood of coronary artery anomalies

  • Juan Francisco Rodriguez Alvarado ,
  • Juan Guzman Olea,
  • Gabriel Guzman Olea,
  • Jorge Guillermo Arenas Fonseca,
  • Zuriel Almeyda Dominguez,
  • Rolando Vicente Colmenares

DOI
https://doi.org/10.24969/hvt.2023.394
Journal volume & issue
Vol. 7, no. 3

Abstract

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Objective: Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA), also known as Bland-White-Garland syndrome, is a rare congenital condition which can manifest as various cardiac symptoms. Case presentation: A 64-year-old male patient presented with functional class deterioration and typical angina to hospital. He was stratified by an ischemia-induced study and underwent coronary angiography that found to have ALCAPA. Conclusions: This is a rare case of ALCAPA due to the patient´s age. Survival to adulthood is possible due to collateral circulation, though the cost is the presence of heart failure, and wherein due to the high surgical risk, in this case optimal medical therapy was decided.

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