Organizing pneumonia as presenting feature of primary Sjögren's syndrome: A case report

Abstract

Sjögren's Syndrome (SS) is an autoimmune inflammatory disease, characterized by lymphocytic infiltration of exocrine glands. Approximately 10% of patients with SS have pulmonary involvement as the first manifestation of their disease, the most common being non-specific interstitial pneumonia.We present the case of a 51-year-old man with organizing pneumonia as the presenting feature of primary SS.Pulmonary involvement as the presenting feature of SS is uncommon, especially when the pattern on CT-scan is that of organized pneumonia. Initial management includes steroids and other immunosuppressants agents, with a better response in organized pneumonia secondary SS cases.

Keywords

• Sjögren syndrome
• Organizing pneumonia
• Bronchoscopy
• Transbronchial biopsy
• Case report