The first successful double switch operation for congenitally corrected transposition of the great arteries in Slovenia

Abstract

Congenitally corrected transposition of the great arteries is a rare congenital heart defect characterized by atrioventricular and ventriculoarterial discordance and can be potentially associated with several other concomitant anomalies, such as ventricular septal defect or congenital complete atrioventricular block. Different surgical options are used for treating the condition. Anatomic repair yields the best long-term outcomes; however, it is technically the most challenging. We present a case of a 3-year old female patient who was electively admitted for complete repair after pulmonary artery banding and pacemaker implantation soon after birth. Subsequently, an anatomic repair (double switch) was performed with an uneventful postoperative course and excellent mid-term outcomes.

Keywords

• congenitally corrected transposition of the great arteries
• ventricular septal defect
• congenital complete atrioventricular block
• double switch procedure
• congenital heart surgery