Primary pigmented nodular adrenocortical disease

Abstract

Primary pigmented nodular adrenocortical disease (PPNAD) is a rare cause of ACTH-independent Cushing′s syndrome and has characteristic gross and microscopic pathologic findings. We report a case of PPNAD in a 15-year-old boy, which was not associated with Carney′s complex. Bilateral adrenalectomy is the treatment of choice.

Keywords

• Cushing′s syndrome
• primary pigmented nodular adrenocortical disease