Macular hole-associated retinal detachment in Best vitelliform dystrophy: Series of two cases and literature review

Abstract

Two eyes of 2 patients with macular hole-associated retinal detachment in clinically diagnosed vitelliruptive stage of Best vitelliform dystrophy were surgically managed by 25-gauge sutureless pars plana vitrectomy, internal limiting membrane (ILM) peeling with inverted ILM flap, and short-acting (SF6) gas tamponade. The patients were assessed with respect to best-corrected visual acuity, color fundus photographs, shortwave fundus autofluorescence, and swept source optical coherence tomography. Surgical intervention led to Type 1 closure of macular hole, resolution of retinal detachment, and improvement in vision in both patients.

Keywords

• Best vitelliform dystrophy
• inverted internal limiting membrane flap
• macular hole
• pars plana vitrectomy
• retinal detachment