Haematologica (Jan 2011)

Red blood cell transfusion-dependency implies a poor survival in primary myelofibrosis irrespective of IPSS and DIPSS

  • Chiara Elena,
  • Francesco Passamonti,
  • Elisa Rumi,
  • Luca Malcovati,
  • Luca Arcaini,
  • Emanuela Boveri,
  • Michele Merli,
  • Daniela Pietra,
  • Cristiana Pascutto,
  • Mario Lazzarino

DOI
https://doi.org/10.3324/haematol.2010.031831
Journal volume & issue
Vol. 96, no. 1

Abstract

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Risk stratification in primary myelofibrosis is currently based on two international prognostic scoring systems, neither of which takes into consideration red blood cell transfusion-dependency. In 288 consecutive patients with primary myelofibrosis, red blood cell transfusion-dependency at diagnosis affects survival independently of the International Prognostic Scoring System (P