Indian Journal of Plastic Surgery (Jan 2010)

Mammoth orbitofrontal neurofibromatosis with herniating meningo-encephalocele

  • Dhanraj Prema,
  • Paul Kingsly,
  • Lamba Shashank,
  • Shetty Rahul

Journal volume & issue
Vol. 43, no. 1
pp. 81 – 83

Abstract

Read online

We are presenting a mammoth orbito-frontal neurofibroma with a herniating meningo-encephalocele in a 23 year old African male. The tumour measured 87cm Χ 54cm and occupied the right orbito-temporo-facial region and had destroyed the right orbit. A pre operative embolization of the feeding vessels was followed by a one stage near total excision of the tumour and repair of the meningo-encephalocele in hypotensive anaesthesia. The excised tumour weighed 8 Kg and, to the best of our knowledge, is the largest orbito-facial neurofibroma reported in literature.

Keywords