A Case of Eosinophilic Granulomatosis with Polyangiitis Complicated with A IgG4 Related Disease Like Symptoms

Suguru Sato; Julia Morimoto; Yasuharu Oguchi; Takashi Umeda; Takaya Kawamata; Mami Rikimaru; Tatsuhiko Koizumi; Ryuichi Togawa; Yasuhito Suzuki; Yuki Sato; Manabu Uematsu; Hiroyuki Minemura; Takefumi Nikaido; Atsuro Fukuhara; Junpei Saito; Kenya Kanazawa; Yoshinori Tanino; Mitsuru Munakata; Yoko Shibata

doi:10.1155/2018/3763084

Case Reports in Immunology (Jan 2018)

A Case of Eosinophilic Granulomatosis with Polyangiitis Complicated with A IgG4 Related Disease Like Symptoms

Suguru Sato,
Julia Morimoto,
Yasuharu Oguchi,
Takashi Umeda,
Takaya Kawamata,
Mami Rikimaru,
Tatsuhiko Koizumi,
Ryuichi Togawa,
Yasuhito Suzuki,
Yuki Sato,
Manabu Uematsu,
Hiroyuki Minemura,
Takefumi Nikaido,
Atsuro Fukuhara,
Junpei Saito,
Kenya Kanazawa,
Yoshinori Tanino,
Mitsuru Munakata,
Yoko Shibata

Affiliations

Suguru Sato: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Julia Morimoto: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Yasuharu Oguchi: Department of Ophthalmology, School of Medicine, Fukushima Medical University, Fukushima, Japan
Takashi Umeda: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Takaya Kawamata: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Mami Rikimaru: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Tatsuhiko Koizumi: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Ryuichi Togawa: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Yasuhito Suzuki: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Yuki Sato: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Manabu Uematsu: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Hiroyuki Minemura: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Takefumi Nikaido: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Atsuro Fukuhara: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Junpei Saito: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Kenya Kanazawa: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Yoshinori Tanino: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan
Mitsuru Munakata: Department of Infectious Disease and Pulmonary Medicine, Aizu Medical Center, Fukushima Medical University, Aizuwakamatsu, Japan
Yoko Shibata: Department of Pulmonary Medicine, School of Medicine, Fukushima Medical University, Fukushima, Japan

DOI: https://doi.org/10.1155/2018/3763084
Journal volume & issue: Vol. 2018

Abstract

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We report a case of eosinophilic granulomatosis with polyangiitis (EGPA) complicated with a IgG4 related disease like symptoms presenting as eyelid swellings. In the present case, the serum level of IgG4 and the ratio of IgG4 to IgG were generally increased by the disease course of EGPA. Considering the course of clinical symptoms, there is a possibility that orbital manifestations were one of the clinical features during the disease course of EGPA while the histological features of right eyelid tissue and other ocular manifestations were consistent with the diagnosis of IgG4 related disease.

Published in Case Reports in Immunology

ISSN: 2090-6609 (Print); 2090-6617 (Online)
Publisher: Wiley
Country of publisher: United Kingdom
LCC subjects: Medicine: Internal medicine: Specialties of internal medicine: Immunologic diseases. Allergy
Website: https://onlinelibrary.wiley.com/journal/1615

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