La Pediatria Medica e Chirurgica (Aug 2014)

Transumbilical laparoscopic treatment of Congenital Infantile Fibrosarcoma of the Ileum

  • G. Scirè,
  • A. Mantovani,
  • N. Zampieri,
  • V.A. Guerriero,
  • D. Segala,
  • S. Pecori,
  • C. Bruno,
  • F.S. Camoglio

DOI
https://doi.org/10.4081/pmc.2014.93
Journal volume & issue
Vol. 36, no. 4

Abstract

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Congenital-Infantile Fibrosarcoma (CIF) is a malignant mesenchymal tumor representing 10-20% of soft-tissue tumors. Complete surgical resection is generally the treatment of choice. The most recurrent cytogenetic abnormality was identified as the traslocation t(12;15)(p13:q25), which bears the fusion of Tel gene EVT6 with TrkC gene. This study describes a case of infantile fibrosarcoma of the ileum in a female newborn examined for intestinal occlusion and its laparoscopic treatment.

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