SA Heart Journal (Apr 2017)

Shone’s complex

  • Farirai F. Takawira,
  • Greenwood Sinyangwe,
  • Michael N. Mwangi,
  • Tshimbiluni M. Mathivha

DOI
https://doi.org/10.24170/7-4-1938
Journal volume & issue
Vol. 7, no. 4
pp. 282 – 286

Abstract

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Shone’s complex is a rare cardiac anomaly consisting of four obstructive lesions of the left heart: supramitral membrane/ring; parachute mitral valve; subaortic stenosis; and coarctation of the aorta. We report on an 18 year-old woman with a variant of Shone’s complex, associated with a large patent ductus arteriosus (PDA ) and pulmonary hypertension. She underwent a successful percutaneous therapeutic catheterisation for the treatment of the coarctation of the aorta and the large PDA using a 45mm covered stent. To our knowledge, this is the first reported case where a covered stent was deployed to treat a native coarctation of the aorta and a PDA in a patient who also had a parachute mitral valve and a bicuspid aortic valve.

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