Clinical Case Reports (Feb 2021)

A case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin

  • Mariarita Sciumè,
  • Fabio Serpenti,
  • Simona Muratori,
  • Valerio Pravettoni,
  • Fabio Massimo Ulivieri,
  • Giorgio Alberto Croci,
  • Anna Chiara Migliorini,
  • Andrea Esposito,
  • Maria Cecilia Goldaniga,
  • Giorgia Natascia Saporiti,
  • Giulia Galassi,
  • Luca Baldini,
  • Francesco Onida,
  • Federica Irene Grifoni

DOI
https://doi.org/10.1002/ccr3.3717
Journal volume & issue
Vol. 9, no. 2
pp. 978 – 982

Abstract

Read online

Abstract Management of systemic mastocytosis is an emerging challenge which requires a multidisciplinary diagnostic approach and personalized treatment strategy. Midostaurin can rapidly reduce the disease burden, also in cladribine refractory cases.

Keywords