Revista de Ciencias Médicas de Pinar del Río (Mar 2018)
Disseminated Superficial Actinic Porokeratosis
Abstract
Introduction: porokeratosis is a hereditary disorder of keratinization. Multiple clinical variants are described, all represented by a common primary lesion: the hyperkeratotic papule. The diagnosis is confirmed with histopathological study, where the cornoid lamella is appreciated, the most representative finding in this dermatosis. The poor response to therapy, the frequent recurrence and its potential preneoplastic nature, make this pathology a complex problem for the dermatologists. One of its variants, the disseminated superficial actinic porokeratosis, is the most frequent clinical form with onset in the third and fourth decades of life, affecting with little predominance the female sex. Objective: to present a case with disseminated superficial actinic porokeratosis (DSAP) confirmed by cutaneous biopsy in a 30-year-old woman. Case report: a woman who comes to the Dermatology Office presenting skin lesions accompanied by intense pruritus located in the upper and lower limbs, mainly in the areas exposed to sunlight, of 2 years of evolution. In the medical interview, it was found that the mother presented the similar skin lesions in photo-exposed areas, whose pathological diagnosis was disseminated superficial actinic porokeratosis. The dermatological physical examination allows suspecting this entity, which is confirmed by biopsy. Conclusions: even though this is a rare entity, the diagnosis can be clinically made considering the symptoms, family history, dermatological physical examination, and the confirmation by means of skin biopsy.
