Long term survival in pediatric hepatic angiosarcoma (PHAS): A case report and review of the literature

Abstract

Pediatric hepatic angiosarcoma (PHAS) is extremely rare, with only five reported tumor-free survivors. Aggressive surgical resection and chemotherapy have been the management in all documented survivors of this disease, however no specific treatment guidelines are established. We present a case of PHAS with the longest reported tumor-free survival at over six years off therapy.

Keywords

• Pediatric hepatic angiosarcoma
• Liver resection
• Liver tumor