Journal of Indian Association of Pediatric Surgeons (Jan 2018)

Persistent mullerian duct syndrome: A single-center experience

  • Saravanan Natarajan,
  • Manikandhan Periasamy,
  • Saminathan Rangasamy,
  • Shankar Mohan,
  • Prabakaran Sundararajan

DOI
https://doi.org/10.4103/jiaps.JIAPS_61_17
Journal volume & issue
Vol. 23, no. 4
pp. 203 – 205

Abstract

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Context: Persistent Mullerian duct syndrome (PMDS) is a rare disorder. It is a type of male pseudohermaphroditism, usually presenting as “Hernia Uteri Inguinalis”. Aims: This study aims to present our experience of PMDS, over a 7-year period. Settings and Design: Our center is a tertiary care facility, situated in Tamil Nadu, a southern state of India. Subjects and Methods: This is a retrospective study. The study period was from 2007 to 2015. Seven cases presented during that period. The difficulties in diagnosis, treatment options discussed, along with a review of literature are presented. Results: Seven cases of PMDS presented over 8 years. Only four were diagnosed preoperatively. Mullerian remnants were excised in five cases. Conclusions: PMDS is rare. Orchiopexy should be the goal of treatment.

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