SAGE Open Medical Case Reports (Nov 2021)

Long-standing necrobiotic xanthogranuloma limited to the skin: A case report

  • Anne-Sophie Smilga,
  • Mona Lavoie,
  • Sungmi Jung,
  • Ariane Schreiber

DOI
https://doi.org/10.1177/2050313X211057929
Journal volume & issue
Vol. 9

Abstract

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Necrobiotic xanthogranuloma is a rare non-Langerhans cell histiocytosis with a known association with monoclonal gammopathies and malignant conditions. There is a lack of consensus regarding the management of necrobiotic xanthogranuloma. In this case report, the patient is diagnosed with a long-standing necrobiotic xanthogranuloma limited to the skin. Although all initial investigations were reassuring, the patient remains at a higher risk of developing a malignant condition. The goal of the authors is to highlight the need for clearer investigation and follow-up guidelines.