Angiomatosis in Klippel-Trenaunay -Weber Syndrome - Report of a rare Case

Abstract

Hemangioma is an abnormal proliferation of blood vessels that may occur in any vascularized tissue. Considerable debate exists as to whether these lesions are neoplasms, hamartomas, or vascular malformations. Hemangiomas occur most often on the skin or in subcutaneous tissue and localized to a single area, but multiple hemangiomas may occur in a single individual, known as hemangiomatosis. Rarely, such hemangiomatosis associated with a variety of pathologies of other organs are seen in Rendu-Osler-Weber syndrome, Sturge-Weber-Dimitri syndrome, Klippel-Trenaunay-Weber syndrome, Maffucci syndrome, von Hippel- Lindau syndrome and Kasabach-Merritt syndrome, which are believed to be within the spectrum of hemangiomatous disease. Hence we report such a rare case of hemangiomatosis seen in a 13 year old boy in association with Klippel-Trenaunay-Weber syndrome.

Keywords

• Hemangioma
• Angiomatosis
• hemangiomatosis
• Klippel-Trenaunay-Weber syndrome