КардиоСоматика (Dec 2022)

A rare case of systemic AL-amyloidosis under the mask of myocardial infarction in the absence of myocardial hypertrophy: case report

  • Svetlana A. Boldueva,
  • Dmitriy S. Evdokimov,
  • Marina V. Rozhdestvenskaya,
  • Sergey A. Vinnichuk,
  • Lyubov B. Mitrofanova

DOI
https://doi.org/10.17816/CS105142
Journal volume & issue
Vol. 13, no. 2
pp. 101 – 106

Abstract

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Systemic amyloidosis is a group of diseases associated with extracellular deposition of fibrillar proteins, resulting in the loss of normal organ structure and function. AL-amyloidosis occurs when amyloid is deposited, consisting of full-length lambda or kappa immunoglobulin light chains, or fragments thereof. This article describes the complexity of timely diagnosis of systemic AL-amyloidosis with a predominant heart lesion in the absence of myocardial hypertrophy on the example of an elderly patient in whom the leading manifestation of the disease was heart failure with a preserved left ventricular ejection fraction.

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