The Pan African Medical Journal (Apr 2021)

Abdominal unicentric Castleman´s disease: a case report

  • Samir Bradai,
  • Amal Khsiba,
  • Abdelwaheb Nakhli,
  • Moufida Mahmoudi,
  • Asma Ben Mohamed,
  • Abir Chaabane,
  • Emna Chelbi,
  • Medhioub Mona,
  • Lamine Hamzaoui,
  • Mousadek Azouz

DOI
https://doi.org/10.11604/pamj.2021.38.339.28859
Journal volume & issue
Vol. 38, no. 339

Abstract

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Castleman´s disease is a rare disease characterized by benign lymphoepithelial proliferation. There are two forms: unicentric and multicentric Castleman´s disease. Mediastinal location is the most frequent. Intra-abdominal Castleman´s disease is a rare presentation. We report a case of 65-year-old female who presented with epigastric pain. Investigations revealed a retroperitoneal mass which was surgically resected. Histopathological examination showed hyaline-vascular type Castleman´s disease. In conclusion, Castelman’s disease is a diagnostic challenge and it must be included in the differential diagnosis of retroperitoneal tumors.

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