Rare Case Report of Angiokeratoma of Tongue: An Uncommon Site

Abstract

Angiokeratoma is an uncommon benign vascular lesion characterized by superficial vascular ectasias along with overlying epidermal acanthosis and hyperkeratosis. In 1889, Mibelli documented the first instance of angiokeratoma on the fingers and toes. In 1896, Fordyce documented the initial instance of angiokeratoma on the scrotum. Isolated oral angiokeratomas are extremely uncommon, and typically they are considered a component of more widespread cutaneous conditions. These papulovascular abnormalities, which range in color from dark red to purple, can have a wide range of dimensions. Fabry’s disease and fucosidosis are two examples of underlying metabolic disorders that frequently coexist with localized or generalized forms of this condition. With the same underlying histology, it presents numerous clinical variations. Angiokeratoma corporis diffusum, a systemic form of the disease, can occasionally cause mucosal involvement, particularly in the oral cavity. In other cases, cutaneous lesions can also be present at other sites. Angiokeratomas of the tongue without any systemic conditions are very rare. Here, we describe a case of angiokeratoma of the tongue in a 14-year-old healthy male patient without any systemic involvement.

Keywords

• acanthosis
• benign vascular lesion
• ectasias