Frontiers in Pediatrics (Oct 2021)

Pulmonary Vein Stenosis: Moving From Past Pessimism to Future Optimism

  • Daniel I. McLennan,
  • Daniel I. McLennan,
  • Elyan C. Ruiz Solano,
  • Elyan C. Ruiz Solano,
  • Stephanie S. Handler,
  • Stephanie S. Handler,
  • Joy Lincoln,
  • Joy Lincoln,
  • Michael E. Mitchell,
  • Michael E. Mitchell,
  • Edward C. Kirkpatrick,
  • Edward C. Kirkpatrick

DOI
https://doi.org/10.3389/fped.2021.747812
Journal volume & issue
Vol. 9

Abstract

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Pulmonary Vein Stenosis (PVS) is a rare disease with a prevalence of around 1. 7 cases per 100,000 children under 2 years old. Treatment options for this disease have not provided great results and pathophysiology of this condition is still poorly understood. Here, we will review the history of PVS including diagnostic tools and treatments, the current management approach, and what the future holds for this devastating disease.

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