Autosomal Dominant Juvenile Amyotrophic LS

Abstract

The clinical and electrodiagnostic findings in 49 affected family members and neuropathological findings from two autopsies of a Maryland kindred with autosomal dominant juvenile amyotrophic lateral sclerosis (ALS) are reported from Johns Hopkins University and Hospital, Baltimore, MD.

Keywords

• amyotrophic lateral sclerosis
• sensory conduction
• dorsal root ganglia