Journal of Tehran University Heart Center (Oct 2021)

Intravenous Leiomyomatosis with Intracardiac Extension as a Rare Cause of Abdominal Pain in an Adult Patient: A Case Report

  • Şahhan Kılıç,
  • Tufan Çınar,
  • Vedat Çiçek,
  • Suha Asal,
  • Murat Selçuk,
  • Muhammed Keskin,
  • Mehtap Güner,
  • Ahmet Turan,
  • Ahmet Lütfullah Orhan

DOI
https://doi.org/10.18502/jthc.v16i4.8605
Journal volume & issue
Vol. 16, no. 4

Abstract

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Intravenous leiomyomatosis (IVL) is a rare and benign smooth muscle tumor that arises from intrauterine venules or the myometrium. We herein describe a 49-year-old woman with a history of myomectomy who developed abdominal pain. An intravascular mass with extension to the right atrium was detected in the inferior vena cava. The mass was surgically resected in a single stage under cardiopulmonary bypass. IVL features were indicated by subsequent histopathology. Postoperatively, the patient was diagnosed with massive pericardial effusion and treated with a pericardial window. At 3 months’ outpatient clinical follow-up, she was asymptomatic. This case indicates that the diagnosis of IVL with extension to the heart should be kept in mind in patients presenting with abdominal pain.

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