A Sporadic Case of Late-onset Vulvar Steatocystoma Multiplex

Abstract

Steatocystoma multiplex is a benign disorder involving the pilosebaceous unit, characterised by the presence of numerous cutaneous cystic lesions in the dermis. While cases with random occurrence are commonly observed, the condition can also be transmitted genetically in an autosomal dominant fashion. The lesions are frequently seen in body parts with a high number of pilosebaceous units including the axillae, scalp, trunk, thighs, arms, and less frequently occurring on the genitals and breasts. Hereby, the authors present a case report of a 48-year-old female who presented to the Outpatient Department of Dermatology with multiple asymptomatic swellings on her vulva since nine years. On physical examination, the swellings were noted to be calcified nodules. These nodules were excised and sent for histopathological analysis that revealed the diagnosis of steatocystoma multiplex. Steatocystoma multiplex can occur as sporadic, familial, or as a part of a syndrome. Although the lesions themselves are symptomless, their presence in the genital region makes walking difficult, thereby hampering routine work and adversely affecting the quality of life of the patient. There is also a need to educate patients regarding its benign nature and possible treatment options. Hence, the present case report aimed to emphasise the importance of its early identification, diagnosis, and to raise awareness among general practitioners.

Keywords

• appendageal neoplasm
• cyst
• histopathology
• subcutaneous nodule