Sporadic angiomyolipoma of the kidney with associated renal vein tumor thrombus

Abstract

Introduction: A renal angiomyolipoma (AML) is a benign kidney tumor that is most often discovered incidentally on imaging. It is generally asymptomatic, benign, and lacks the potential for invasion or metastasis. Case Presentation: Herein we discuss the presentation and management of an 83-year-old male who was incidentally discovered to have a renal AML of the right kidney with renal vein tumor thrombus. On presentation, computed tomography (CT) scan demonstrated a centralized AML of the right kidney with an associated fatty tumor thrombus of the renal vein extending to the renal vein ostium. The patient subsequently underwent exploratory laparotomy, right radical nephrectomy, venous tumor thrombectomy, and primary cavorraphy and recovered without complication. Follow-up surveillance imaging demonstrated complete removal of the tumor. Conclusion: Radical nephrectomy with tumor thrombectomy remains the gold standard approach to surgical intervention regarding angiomyolipomas with a tumor thrombus. Micro Abstract: This is a case report of an 83-year-old male demonstrating a rare presentation of a renal angiomyolipoma associated with a renal vein tumor thrombus. The tumor was found incidentally on imaging and was later resected. Herein, we discuss treatment strategy and outcomes for angiomyoliopoma with venous tumor thrombus.

Keywords

• Angiomyolipoma
• Kidney
• Venous tumor thrombus
• Inferior vena cava
• Thrombectomy