Bilateral Adrenal PNET: A Rare Presentation

Abstract

Primitive neuroectodermal tumours or PNET's are rare, malignant tumours with aggressive course and extremely poor prognosis. They have no sex preference. They arise mostly in the second decade of life. They are believed to be of neural crest origin and carry the name primitive because majority of the neuronal cells in these tumours appear undifferentiated. Solid organ origin is very rare and tumours arising from the adrenals are very infrequent. We report a case of metastatic bilateral adrenal PNET in a 45-year-old man. We believe this to be the first such case reported in the urological literature.

Keywords

• adrenal tumour
• neural crest origin
• primitive neuroectodermal tumour