Clinical Case of the Complete Form of Androgen Insensitivity Syndrome (AIS)

Abstract

The article presents a clinical observation of an extremely rare in gynecological practice androgen insensitivity syndrome (AIS). The authors give data on the pathogenesis of the disease, modern classification and terminology of various forms of this pathology. The phenotypic manifestations of the disease, the results of clinical and instrumental studies and surgical treatment are described.The results of the study show the possibility of clinical diagnosis of AIS and timely surgical treatment of patients with this pathology, due to the high risk of gonadal malignancy.

Keywords

• androgen insensitivity syndrome
• testicular feminization syndrome
• morris syndrome
• disorder of sex development
• gonadectomy
• hormone replacement therapy