Ventricular septal defect with pulmonary arterial hypertension in an infant: Is there something more than what meets the eye?

Abstract

An 11-month-old girl was detected to have muscular ventricular septal defect with hyperkinetic pulmonary hypertension (PH) was urgently operated upon. On follow-up, her PH worsened, resulting in right ventricular dysfunction and was later detected to have absent portal vein.

Keywords

• absent portal vein
• pulmonary hypertension
• ventricular septal defect