Juvenile Familial Amyotrophic Lateral Sclerosis

Abstract

Four cases of JFALS in a family, with mean age at onset of 15.7 years and exceptionally long survival (mean, 27 years), are reported from the National Institute of Neurology and Neurosurgery, Mexico City.

Keywords

• cognitive deterioration
• classic pyramidal degeneration
• dementia in adulthood