Auditory neuropathy spectrum disorder in a patient with normal hearing and its medical management: case presentation and literature review

Abstract

Auditory neuropathy spectrum disorder (ANSD) is a group of alterations of the auditory system that manifests the presence of otoacoustic emissions and the absence of responses in auditory brainstem response. However, because these patients can have a very diverse clinical presentation, their management is very complex. Patients can present from normal hearing with practically normal development, to profound hearing loss with various comorbidities that require a highly individualized approach. Early detection and close follow-up of ANSD should be a priority to avoid iatrogenic management.

Keywords

• Auditory neuropathy spectrum disorder; Auditory brainstem response; Otoacoustic emissions; Automated auditory brainstem response