A rare case of diagnosed absent aortic valve and severely hypoplastic pulmonary valve with double outlet right ventricle: A case report
V.V. Suvorov,
E.P. Fedotova,
V.V. Zaitsev,
E.V. Dolgova,
L.L. Popova,
A.E. Glazunova,
M.U. Novak,
R.A. Nasyrov
Affiliations
V.V. Suvorov
Department of Surgical Diseases of Children, Saint Petersburg State Pediatric Medical University, Saint-Petersburg, 194100, Russia; Corresponding author.
E.P. Fedotova
Department of Pathological Anatomy, Saint Petersburg State Pediatric Medical University, Saint-Petersburg, 194100, Russia
V.V. Zaitsev
Department of Surgical Diseases of Children, Saint Petersburg State Pediatric Medical University, Saint-Petersburg, 194100, Russia
E.V. Dolgova
Department of Anaesthesia and Intensive Care for Children with Cardiac Pathology, Saint Petersburg State Pediatric Medical University, Saint-Petersburg, 194100, Russia
L.L. Popova
Department of Anaesthesia and Intensive Care for Children with Cardiac Pathology, Saint Petersburg State Pediatric Medical University, Saint-Petersburg, 194100, Russia
A.E. Glazunova
Department of Pathology of Newborns and Premature Babies, Saint Petersburg State Pediatric Medical University, Saint-Petersburg, 194100, Russia
M.U. Novak
Department of Anaesthesia and Intensive Care for Children with Cardiac Pathology, Saint Petersburg State Pediatric Medical University, Saint-Petersburg, 194100, Russia
R.A. Nasyrov
Department of Pathological Anatomy, Saint Petersburg State Pediatric Medical University, Saint-Petersburg, 194100, Russia
Agenesis of the aortic and pulmonary valves is a very rare congenital malformation of the semilunar valves. The literature describes no more than thirty cases of such anomaly in combination with congenital heart disease. Most descriptions include aplasia of either the aortic or pulmonic valve. The combination of such defect in both valves has been described in a much smaller number of scientific papers.In this article, we present a clinical case of the treatment of a patient with agenesis of aortic valve and severely hypoplastic pulmonary valve. As a result circulatory arrest occurred immediately after birth, which required the implementation of cardiopulmonary resuscitation. The child was resuscitated and transferred to the intensive care unit for further examination and treatment.
