Full-mouth Rehabilitation of an Amelogenesis Imperfecta Case with Skeletal Open Bite

Abstract

Introduction: Amelogenesis imperfect (AI) refers to a group of autosomal dominant disorders primarily affecting the enamel and can present a variety of clinical appearances. This report describes a multidisciplinary approach for oral rehabilitation of a young man patient with hypoplastic AI with severe skeletal anterior open bite (AOB). Case Report: A 22-year-old male patient was presented with compromised masticatory efficiency and dissatisfaction with his teeth appearance. Based on the clinical and radiographic examination, the patient was confirmed as AI (hypoplastic type) with severe AOB. The treatment included orthognathic surgery (Le Fort I osteotomy and genioplasty) for correcting AOB, long face, and limited space in the posterior region, followed by crown lengthening and prosthetic rehabilitation. Before surgery, a mock-up of all teeth was performed to facilitate alignment and stabilization of the dental arches during the Le Fort I osteotomy. Results: Solid tooth interdigitation that provided with mock-up, helped to adjust the stable skeletal position of the maxilla during the surgery. Conclusion: preoperative mock-up appears to be an efficient fixation option to achieve an acceptable occlusion after prosthetic rehabilitation in AI patients with severe AOB.

Keywords

• amelogenesis imperfecta, open bite, orthognathic surgery, dental prosthesis