The conundrum of post-traumatic corneal rupture in a patient with Ehlers-Danlos syndrome

Abstract

To describe the management of post-traumatic Descemet’s membrane detachment and intraoperative corneal rupture in a known case of Ehlers-Danlos Syndrome (EDS). A 7-year-old child, a known case of EDS, presented with Descemet’s membrane tear in the right eye for which intracameral sulfur hexafluoride (SF6) and descemetopexy were done. Intraoperative spontaneous rupture of the cornea was noted during descemetopexy which was managed using cyanoacrylate glue and bandage contact lens. We successfully used cyanoacrylate tissue adhesive glue for sealing of corneal rupture suggesting that it can be considered a treatment option for such cases where there is a lack of tissue strength for suturing.

Keywords

• acute hydrops
• cyanoacrylate glue
• descemetopexy
• ehlers–danlos syndrome