Bilateral anterior lenticonus in Alport syndrome

Abstract

Anterior lenticonus is a structural anomaly of the crystalline lens characterized by a localized conical or spherical protrusion centered about the pole of the anterior lens surface. A 23-year-old female presented with a gradual, progressive, painless decrease in vision of both eyes associated with hearing loss from childhood. The anterior segment examination showed a conical protrusion of the lens in the pupillary axis. Fundus showed pigmentary changes and a dull foveolar reflex-lozenge sign. Clear lens extraction was done for both eyes. The central protruded fragile lens capsule was meticulously handled during surgery to create well centered circumcorneal capsulorhexis using micro forceps.

Keywords

• astigmatism
• lenticonus
• lozenge sign